einstein (São Paulo). 22/Mar/2022;20:eRW5686.

Brazilian Guidelines for Nutrition in Cystic Fibrosis

Lenycia de Cassya Lopes , Miriam Isabel Souza dos Santos , Valéria Laguna Salomão , Eliana , Monique Ferreira , Juliana Ferreira , Renata Rodrigues , Mirella Aparecida , Carolina de Azevedo Pedrosa , Marcelo Coelho , Anna Carolina Di Creddo , Jocemara , Maria de Fatima , Matias , Rodrigo

DOI: 10.31744/einstein_journal/2022RW5686

ABSTRACT

Objective

To develop a scientific consensus on nutrition in cystic fibrosis.

Methods

Sixteen coordinators elaborated relevant questions on nutritional therapy in cystic fibrosis, which were divided into six sections: nutritional assessment, nutritional recommendations, nutritional intervention, dietary counseling, special situations and enzyme replacement, and gastrointestinal manifestations. Two to three specialists in the field were responsible for each section and obtaining answers formulated based on standardized bibliographic searches. The available literature was searched in the PubMed®/MEDLINE database, after training and standardization of search strategies, to write the best level of evidence for the questions elaborated. Issues related to disagreement were discussed until a consensus was reached among specialists, based on the current scientific literature.

Results

Forty-two questions were prepared and objectively answered, resulting in a consensus of nutritional therapy in cystic fibrosis.

Conclusion

This work enabled establishing a scientific consensus for nutritional treatment of cystic fibrosis patients.

Brazilian Guidelines for Nutrition in Cystic Fibrosis
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