einstein (São Paulo). 20/Dec/2019;18:eRC5111.

Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review

Carolina Rodrigues Dal , Beatriz Piovesana , Leticia Piovesana , Gabriella Paes del , Nelson

DOI: 10.31744/einstein_journal/2020RC5111

ABSTRACT

Situs inversus totalis is a rare recessive autosomal congenital abnormality in which the mediastinal and abdominal organs are in a mirrored position when compared to the usual topography. The literature reports some cases of situs inversus totalis and concomitant conditions: spinal abnormalities, cardiac malformations and hematological diseases, such as idiopathic thrombocytopenic purpura, which is an autoimmune disease that causes thrombocytopenia due to platelet destruction or suppression of its production. This article aimed to report the coexistence of situs inversus totalis and idiopathic thrombocytopenic purpura.

Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review
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